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Magnetic resonance imaging of arrhythmogenic dysplasia of the right ventricle


Authors: Makarenko V.N., Shlyappo M.A., Aleksandrova S.A.

Company:
Bakoulev National Medical Research Center for Cardiovascular Surgery, Rublevskoe shosse, 135, Moscow, 121552, Russian Federation

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Heading: Clinical Cases

UDC: 616.12-073.75:616.124

Link: Clinical Physiology of Blood Circulaiton. 2019; 4 (3): 280-282

Quote as: Makarenko V.N., Shlyappo M.A., Aleksandrova S.A. Magnetic resonance imaging of arrhythmogenic dysplasia of the right ventricle. Cardiovascular Surgery News. 2019; 3 (4): 280–2 (in Russ.). DOI: 10.24022/ 2588-0284-2019-3-4-280-282

Received / Accepted:  20.11.2019 / 30.11.2019

Full text:  


Abstract

In 1977–1982 G. Fontaine et al. presented descriptions of primary cardiomyopathy – arrhythmogenic dysplasia of the right ventricle (ARVC), as cases of sudden death in young people with right ventricular tachycardia. Mutations of desmosome proteins, the main elements of the intercellular adhesion structures present in the myocardium, are the most common genetic cause of ARVC.

In 1994, the Working Group criteria (TFC) were approved for the diagnosis of ARVC, in 2010, the criteria were revised. The most important include changes in the right chest leads on the electrocardiogram, signs of dilatation of the pancreas with local dyskinesias according to echocardiography and magnetic resonance imaging, stable ventricular tachycardia from the right ventricle, fibrous or fibro-fatty myocardial replacement and the detection of specific mutations.

References

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  2. Голухова Е.З., Громова О.И., Шомахов Р.А., Булаева Н.И., Бокерия Л.А. Моногенные аритмические синдромы: от молекулярно-генетических аспектов к постели больного. Acta Naturae (русскоязычная версия). 2016; 8 (29): 70–83. [Golukhova E.Z., Gromova O.I., Shomakhov R.A., Bulaeva N.I., Bockeria L.A. Monogenec arrhythmic syndromes: from molecular and genetic aspects to bedside. Acta Naturae. 2016; 8 (29): 70–83 (in Russ.).]

About Authors

  • Vladimir N. Makarenko, Dr. Med. Sc., Professor, Head of Department, ORCID
  • Mariya A. Shlyappo, Cand. Med. Sc., Radiologist,ORCID
  • Svetlana A. Aleksandrova, Cand. Med. Sc., Senior Researcher, ORCID

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