Логотип НМИЦССХ им. А.Н. Бакулева Журнал «Новости сердечно-сосудистой хирургии»





2019; 3 (4) 

Клинические рекомендации по ведению пациентов с атрезией трехстворчатого клапана (пересмотр 2019 года)

Авторы: Рабочая группа АССХ России: Бокерия Л.А. (академик РАН и РАМН), Гущин Д.К. (науч. сотр.), Зеленикин М.М. (д.м.н., профессор), Арнаутова И.В. (д.м.н.), Волков С.С. (к.м.н.), Горбачевский С.В. (д.м.н., профессор), Зеленикин М.А. (д. м. н., профессор), Ким А.И. (д.м.н., профессор), Кокшенев И.В. (д.м.н., профессор), Купряшов А.А. (д.м.н.), Никифоров А.Б. (мл. науч. сотр.), Подзолков В.П. (академик РАН), Свободов А.А. (д.м.н.), Шаталов К.В. (д.м.н., профессор), Шмальц А.А. (д.м.н.), Юрлов И.А. (к.м.н.).

Организация:
ФГБУ «Национальный медицинский исследовательский центр сердечно-сосудистой хирургии им. А.Н. Бакулева» (директор – академик РАН и РАМН Л.А. Бокерия) Минздрава России, Рублевское ш., 135, Москва, 121552, Российская Федерация

Для корреспонденции: Сведения доступны для зарегистрированных пользователей.

Раздел: Клинические рекомендации

DOI: https://doi.org/10.24022/2588-0284-2019-3-4-258-276

УДК: 616.126

Библиографическая ссылка: Новости сердечно-сосудистой хирургии. 2019; (3): 258-276

Цитировать как: Рабочая группа АССХ России: Бокерия Л.А. (академик РАН и РАМН), Гущин Д.К. (науч. сотр.), Зеленикин М.М. (д.м.н., профессор), Арнаутова И.В. (д.м.н.), Волков С.С. (к.м.н.), Горбачевский С.В. (д.м.н., профессор), Зеленикин М.А. (д. м. н., профессор), Ким А.И. (д.м.н., профессор), Кокшенев И.В. (д.м.н., профессор), Купряшов А.А. (д.м.н.), Никифоров А.Б. (мл. науч. сотр.), Подзолков В.П. (академик РАН), Свободов А.А. (д.м.н.), Шаталов К.В. (д.м.н., профессор), Шмальц А.А. (д.м.н.), Юрлов И.А. (к.м.н.).. Клинические рекомендации по ведению пациентов с атрезией трехстворчатого клапана (пересмотр 2019 года). Новости сердечно-сосудистой хирургии. 2019; (3): 258-276. DOI: 10.24022/2588-0284-2019-3-4-258-276

Ключевые слова: атрезия трехстворчатого клапана; врожденные пороки сердца; клинические рекомендации

Полнотекстовая версия:  

Аннотация

Атрезия трехстворчатого клапана – сложный врожденный порок сердца, при котором правое предсердие не открывается в правый желудочек через правый атриовентрикулярный клапан. Частота встречаемости порока среди всех врожденных аномалий сердца составляет 1,1–3,1%, при этом он занимает третье место по распространенности среди пороков «синего» типа. Прогноз естественного течения атрезии трехстворчатого клапана неблагоприятный: без операции на первом году жизни умирают до 67%, а к 10 годам – до 90% детей. Настоящие клинические рекомендации отражают современные представления об этиопатогенезе, клинической картине, диагностике, консервативном и хирургическом лечении пациентов с атрезией трехстворчатого клапана. Отдельно рассмотрен вопрос лекарственной тромбопрофилактики после этапного хирургического лечения.

Литература

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